Sindromy Zhil'bera, Dubina-Dzhonsona : i drugie formy khronicheskikh semeynykh ne gemoliticheskikh giperbilirubinemiy

V monografii izlozheny patogenez, klinika, diagnostika i lechenie khronicheskikh semeynykh ne gemoliticheskikh giperbilirubinemiy: sindromov Kriglera-Nayyara, Zhil'bera, Dubina-Dzhonsona, Rotora, Lyusi-Driskoll, Aagenesa, Baylera i dr. Issledovanie sistemy immuniteta pri sindromakh Zhil'bera i Dubina-Dzhonsona pozvolilo ustanovit' nalichie immunodefitsita po kletochnomu tipu, chto, vozmozhno i obuslovlivaet vysokuyu chastotu markerov virusnoy infektsii (HBV) pri etikh formakh khronicheskikh semeynykh ne gemoliticheskikh giperbilirubinemiy. S novykh pozitsiy rassmatrivayutsya perspektivy issledovaniya i profilaktiki nasledstvennykh form narusheniya obmena bilirubina.